Is Hepatolenticular Degeneration a Clinico-Pathological Entity ?
نویسندگان
چکیده
منابع مشابه
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متن کاملHepatolenticular Degeneration (Wilson's Disease)
A R?eport of five cases, with Commentary WILSON'S disease is a heredo-familial disorder, the essential pathological elements of which consist in a cirrhotic state of the liver comb;ned with degenerative changes in the lenticular nuclei of the brain. The term "hepatolenticular degenera-tion" is therefore aptly precise, but affords little clue to the diversity of the clinical manifestations. A lo...
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متن کاملWilson's disease; hepatolenticular degeneration.
The inclusion of a rare neurological disease in an issue of this journal devoted to disorders of the liver would seem to warrant some explanation for although cirrhosis of the liver is an integral part of the syndrome of Wilson's disease, it accounts for an insignificant proportion of all patients suffering from hepatic cirrhosis. However, although quantitatively unimportant, its significance r...
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ژورنال
عنوان ژورنال: Proceedings of the Royal Society of Medicine
سال: 1954
ISSN: 0035-9157
DOI: 10.1177/003591575404700218